Jornal Britânico de Pesquisa Acesso livre

Abstrato

The Pulmonary involvement as the initial manifestation of Pediatric Sjögren

Sieiro Santos

Sjögren’s syndrome is a systemic autoimmune disease caused by lymphocytic infiltration of exocrine glands causing sicca syndrome. It can affect extra-glandular or­gans such as the lungs which can result in diffuse intersti­tial lung disease, a well-known form of lung involvement.

In pediatric patients, Sjögren’s syndrome is less common that in adult patients and often associates more heteroge­neous presentations.